Publicado

2022-08-03

Folliculitis decalvans: a case report of satisfactory recovery after implementing isotretinoin therapy

Foliculitis decalvante. Reporte de un caso con recuperación satisfactoria mediante tratamiento con isotretinoina

Folliculitis decalvans: Um relato de caso em um trabalhador de saúde de 26 anos de idade

DOI:

https://doi.org/10.15446/cr.v8n1.88800

Palabras clave:

Folliculitis, Hair Follicle, Isotretinoin, Cicatricial alopecia (en)
Foliculitis, Isotretinoina, Folículo piloso, Alopecia (es)

Autores/as

Introduction: Folliculitis decalvans is a rare skin disease characterized by the presence of painful papules and pustules with an underlying neutrophilic infiltrate, usually on the scalp. Its treatment is lengthy and challenging, and recurrence is relatively common. Although its etiology is unknown, several theories explaining its development have been proposed, including colonization by Staphylococcus aureus.

Case description: This is the case of a 26-year-old male healthcare worker who visited the outpatient service after experiencing a 4-year history of painful pustules on the scalp; initially these lesions were located in the occipital region, but then also started to appear in the temporal and parietal regions. After being treated for bacterial folliculitis and having several recurrences, a skin biopsy was performed, which allowed diagnosing him with folliculitis decalvans. Once the diagnosis was made, isotretinoin (20mg) treatment was implemented for a year and a half, achieving complete remission of the lesions.

Conclusion: Although this case has some limitations, such as the lack of histopathology images and some control laboratory tests, it clearly shows the difficulties faced when treating this type of skin disorders and presents an overview of the use of isotretinoin, evidencing that although this drug is well tolerated, possible adverse reactions from drug interactions with trimethoprim/sulfamethoxazole may arise. In addition, this case is of great importance since the possible presence of a familial cluster of folliculitis decalvans could be confirmed, if further genetic testing is performed.

Introducción. La folliculitis decalvans es una enfermedad dermatológica rara caracterizada por la presencia de pápulas y pústulas dolorosas que están acompañadas de un infiltrado de neutrófilos subyacente. Esta condición suele aparecer en el cuero cabelludo, su recurrencia es relativamente común y su tratamiento, largo y difícil. Aunque su etiología es desconocida, se han propuesto muchas teorías que intentan explicar su aparición, siendo la colonización por Staphylococcus aureus una de ellas.

Presentación del caso. Hombre de 26 años que se desempeñaba como trabajador de la salud y consultó por un cuadro clínico de 4 años de evolución caracterizado por la aparición de pústulas dolorosas en la región occipital, las cuales, posteriormente se extendieron a la región temporal y parietal. Después de tratarlo como una foliculitis infecciosa y tras múltiples recurrencias, se realizó una biopsia de las lesiones que permitió diagnosticarlo con folliculitis decalvans. Se instauró un tratamiento consistente de 20mg de isotretinoina al día por un año y medio, con el cual se logró la resolución de la folicutis. Sin embargo, dos años después tuvo un relapso, pero, según el paciente, esto pudo ocurrir por el consumo de derivados lácteos, ya que, según indicó, cuando suspende el consumo de esta clase de productos no aparecen más lesiones luego de 2-3 semanas..

Conclusión. Aunque este caso tiene algunas limitaciones como la ausencia de imágenes histopatológicas y algunos laboratorios de control, muestra las dificultades para tratar este tipo de condiciones dermatológicas y presenta un panorama del uso de la isotretinoina, ya que evidencia que este medicamento tiene una buena tolerancia, pero presenta interacciones medicamentosas adversas con la trimetoprima/sulfametoxazol. Además, este caso es de gran importancia, ya que, si se realizan más pruebas genéticas. podría confirmarse la posible presencia de un grupo familiar de foliculitis decalvante.

Introdução: A foliculite decalvante é uma doença dermatológica rara, caracterizada por pápulas e pústulas dolorosas com um infiltrado neutrofílico subjacente, ocorrendo geralmente no couro cabeludo. Seu tratamento é difícil e demorado. A recorrência é relativamente comum. Várias teorias têm sido propostas, incluindo a colonização por Staphylococcus aureus. Aqui é relatado um caso de foliculite decalvante em um trabalhador da saúde.
Descrição do caso: Um trabalhador de saúde masculino de 26 anos descreve uma história clínica de quatro anos de pústulas e pápulas de início insidioso, aparecendo inicialmente na região occipital e depois distribuindo para as regiões temporal e occipital. Após tratamento para outras condições infecciosas e sem várias recidivas, foi feita uma biópsia das lesões. Esta biópsia foi compatível com o diagnóstico de Folliculitis decalvans. Após a biópsia, ele foi tratado com Isotretinoína 20mg durante um ano e meio com remissão completa.
Discussão: Este caso expõe claramente as dificuldades de tratar este tipo de condições dermatológicas, requer paciência e uma grande quantidade de recursos. Este caso é importante, pois mostra sinais e sintomas comuns. Uma análise mais aprofundada do histórico genético e da condição imunológica do paciente pode ser aconselhável.
Conclusão: A foliculite decalvante é difícil de diagnosticar e tratar. Vários tratamentos podem ser necessários. A recorrência é sempre uma possibilidade.

Referencias

Whiting DA. Cicatricial alopecia: clinico-pathological findings and treatment. Clin Dermatol. 2001;19(2):211-25. https://doi.org/brbth4 .

Vañó‐Galván S, Molina‐Ruiz AM, Fernández‐Crehuet P, Rodrigues‐Barata A, Arias‐Santiago S, Serrano‐Falcón C, et al. Folliculitis decalvans: a multicentre review of 82 patients. J Eur Acad Dermatol Venereol. 2015;29(9):1750-7. https://doi.org/f8qkw9 .

Olsen EA, Bergfeld WF, Cotsarelis G, Price VH, Shapiro J, Sinclair R, et al. Summary of North American Hair Research Society (NAHRS)-sponsored workshop on cicatricial alopecia, Duke university medical center, February 10 and 11, 2001. J Am Acad Dermatol. 2003;48(1):103-10. https://doi.org/bf2k5p .

Forman L. Folliculitis Decalvans (de Quinquad). J R Soc Med. 1943;36(6):295. https://doi.org/hfs9 .

Otberg N, Kang H, Alzolibani AA, Shapiro J. Folliculitis decalvans. Dermatol Ther. 2008;21(4):238-44. https://doi.org/cxpbqd .

Powell JJ, Dawber RP, Gatter K. Folliculitis decalvans including tufted folliculitis: clinical, histological and therapeutic findings. Br J Dermatol. 1999;140(2):328-33. https://doi.org/d2w5bc .

Annessi G. Tufted folliculitis of the scalp: a distinctive clinicohistological variant of folliculitis decalvans. Br J Dermatol. 1998;138(5):799-805. https://doi.org/czj2q3 .

Chandrawansa PH, Giam YC. Folliculitis decalvans a retrospective study in a tertiary referred centre, over five years. Singapore Med J. 2003;44(2):84-7.

Sillani C, Bin Z, Ying Z, Zeming C, Jian Y, Xingqi Z. Effective treatment of folliculitis decalvans using selected antimicrobial agents. Int J Trichology. 2010;2(1):20-3. https://doi.org/frxqgr

Jaiswal AK, Vaishampayan S, Walia NS, Verma R. Folliculitis decalvans in a family. Indian J Dermatol Venereol Leprol. 2000;66(4):216-7.

Douwes KE, Landthaler M, Szeimies RM. Simultaneous occurrence of folliculitis decalvans capillitii in identical twins. Br J Dermatol. 2000;143(1):195-7. https://doi.org/fxf3hb .

Collier NJ, Allan D, Diaz-Pesantes F, Sheridan L, Allan E. Systemic photodynamic therapy in folliculitis decalvans. Clin Exp Dermatol. 2018;43(1):46-9. https://doi.org/hf5r .

Ross EK, Tan E, Shapiro J. Update on primary cicatricial alopecias. J Am Acad Dermatol. 2005;53(1):1-37. https://doi.org/dcm8sg .

Rudnicka L, Olszewska M, Rakowska A, Slowinska M. Trichoscopy update 2011. J Dermatol Case Rep. 2011;5(4):82-8. https://doi.org/dpjtvg .

Fabris MR, Melo CP, Melo DF. Folliculitis decalvans: the use of dermatoscopy as an auxiliary tool in clinical diagnosis. An Bras Dermatol. 2013;88(5):814-6. https://doi.org/gcbvdj .

Rakowska A, Stefanato C, Czuwara J, Olszewska M, Rudnicka L. Folliculitis Decalvans. In: Rudnicka L, Olszewska M, Rakowska A, editors. Atlas of Trichoscopy: Dermoscopy in Hair and Scalp Disease. London: Springer London; 2012. p. 319-29. https://doi.org/hf5s .

Inui S. Trichoscopy for common hair loss diseases: algorithmic method for diagnosis. J Dermatol. 2011;38(1):71-5. https://doi.org/dv3c65 .

Chiarini C, Torchia D, Bianchi B, Volpi W, Caproni M, Fabbri P. Immunopathogenesis of folliculitis decalvans: clues in early lesions. Am J Clin Pathol. 2008;130(4):526-34. https://doi.org/c89hqh .

Brooke RC, Griffiths CE. Folliculitis decalvans. Clin Exp Dermatol. 2001;26(1):120-2. https://doi.org/dtppm8 .

Miguel-Gómez L, Rodrigues-Barata AR, Molina-Ruiz A, Martorell-Calatayud A, Fernández-Crehuet P, Grimalt R, et al. Folliculitis decalvans: effectiveness of therapies and prognostic factors in a multicenter series of 60 patients with long-term follow-up. J Am Acad Dermatol. 2018;79(5):878-83. https://doi.org/gfhcjt .

Miguel-Gomez L, Vano-Galvan S, Perez-Garcia B, Carrillo-Gijon R, Jaen-Olasolo P. Treatment of folliculitis decalvans with photodynamic therapy: Results in 10 patients. J Am Acad Dermatol. 2015;72(6):1085-7. https://doi.org/f3gqdr .

Tedesco M. Adipose tissue transplant in recurrent folliculitis decalvans. Int J Immunopathol Pharmacol. 2018;32: 2058738418814688. https://doi.org/hf5v .

Tietze JK, Heppt MV, Von Preußen A, Wolf U, Ruzicka T, Wolff H, et al. Oral isotretinoin as the most effective treatment in folliculitis decalvans: a retrospective comparison of different treatment regimens in 28 patients. J Eur Acad Dermatol Venereol. 2015;29(9):1816-21. https://doi.org/f8qmt3 .

Mihaljević N, von den Driesch P. Successful use of infliximab in a patient with recalcitrant folliculitis decalvans. J Deutsch Dermatol Ges. 2012;10(8):589-90. https://doi.org/hf5w .

Camacho F. Alopecias cicatriciales. En Tricología: Enfermedades del Folículo Pilosebáceo. 1996. Aula Medica Madrid.

Meesters AA, Van der Veen JP, Wolkerstorfer A. Long-term remission of folliculitis decalvans after treatment with the long-pulsed Nd:YAG laser. J Dermatolog Treat. 2014;25(2):167-8. https://doi.org/hf5x .

Yeh JE, Hartman RI, Xu J, Hoang M, Yasuda MR. Resolution of folliculitis decalvans with medical honey. Dermatol Online J. 2019;25(8):13030/qt07n6v0hs. https://doi.org/hf5z .

Trüeb R. [Cicatricial alopecias]. Hautarzt. 2013;64(11):810-9. https://doi.org/hf52 .

Headington JT. Transverse microscopic anatomy of the human scalp: a basis for a morphometric approach to disorders of the hair follicle. Arch Dermatol. 1984;120(4):449-56. https://doi.org/dn4b97 .

Wolff H, Fischer TW, Blume-Peytavi U. The diagnosis and treatment of hair and scalp diseases. Dtsch Ärztebl Int. 2016;113(21):377-86. https://doi.org/hf53 .

Stockmeier M, Kunte C, Feldmann K, Messer G, Wolff H. Folliculitis decalvans-Behandlung mit einer systemischen Rifampicin-Clindamycin-Kombinationstherapie bei 17 Patienten. Akt Dermatol. 2001;27:361-3.

Bolz S, Jappe U, Hartschuh W. Successful treatment of perifolliculitis capitis abscedens et suffodiens with combined isotretinoin and dapsone. J Dtsch Dermatol Ges. 2008;6(1):44-7. https://doi.org/brqvgf

Kossard S. Postmenopausal frontal fibrosing alopecia: scarring alopecia in a pattern distribution. Arch Dermatol. 1994;130(6):770-4. https://doi.org/brzmrx .

Vañó-Galván S, Molina-Ruiz AM, Serrano-Falcón C, Arias-Santiago S, Rodrigues-Barata AR, Garnacho-Saucedo G, et al. Frontal fibrosing alopecia: a multicenter review of 355 patients. J Am Acad Dermatol. 2014;70(4):670-8. https://doi.org/f2q5f7 .

Harries MJ, Messenger A. Treatment of frontal fibrosing alopecia and lichen planopilaris. J Eur Acad Dermatol Venereol. 2014;28(10):1404-5. https://doi.org/hf54 .

Le Cleach L, Chosidow O. Clinical practice. Lichen planus. N Engl J Med. 2012;366(8):723-32. https://doi.org/gnz7w7 .

Tan E, Martinka M, Ball N, Shapiro J. Primary cicatricial alopecias: clinicopathology of 112 cases. J Am Acad Dermatol. 2004;50(1):25-32. https://doi.org/d98scc .

Bunagan MJ, Banka N, Shapiro J. Retrospective review of folliculitis decalvans in 23 patients with course and treatment analysis of long-standing cases. J Cutan Med Surg. 2015;19(1):45-9. https://doi.org/f67rbq .

Aksoy B, Hapa A, Mutlu E. Isotretinoin treatment for folliculitis decalvans: a retrospective case‐series study. Int J Dermatol. 2018;57(2):250-3. https://doi.org/gcsxd5 .

Rambhia PH, Conic RRZ, Murad A, Atanaskova-Mesinkovska N, Piliang M, Bergfeld W. Updates in therapeutics for folliculitis decalvans: A systematic review with evidence-based analysis. J Am Acad Dermatol. 2019;80(3):794-801. https://doi.org/hf56 .

Lugović-Mihić L, Barisić F, Bulat V, Buljan M, Situm M, Bradić L, et al. Differential diagnosis of the scalp hair folliculitis. Acta Clin Croat. 2011;50(3):395-402.

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Foliculitis decalvante. Reporte de un caso con recuperación satisfactoria mediante tratamiento con isotretinoina. (2022). Case Reports, 8(1), 9-23. https://doi.org/10.15446/cr.v8n1.88800