Publicado

2015-01-01

Linfoma T Intestinal Monomórfico CD56+. Primer Caso Informado en Colombia y Revisión de la Literatura

Monomorphic Intestinal T-Cell Lymphoma. First reported case in Colombia and review of the literature

Palabras clave:

linfoma de células T, linfoma T asociado a enteropatía, CD56 (es)
Lymphoma T-cell, Enteropathy-Associated T-Cell Lymphoma, Small bowel, Antigens CD56 (en)

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Autores/as

  • Diana Lucía Martínez-Baquero Departamento de Patología, Grupo de Patología Molecular, Facultad de Medicina, Universidad Nacional de Colombia. Bogotá, D. C., Colombia.
  • Leandro Galvis-Moreno Laboratorio de Patología, Clínica San José. Cúcuta, Colombia.
  • Jinneth Acosta-Forero Departamento de Patología, Grupo de Patología Molecular, Facultad de Medicina, Universidad Nacional de Colombia. Bogotá, D. C., Colombia.
  • Orlando Ricaurte-Guerrero Departamento de Patología, Grupo de Patología Molecular, Facultad de Medicina, Universidad Nacional de Colombia. Bogotá, D. C., Colombia.

Se informa el caso de una mujer de 80 años con hallazgo incidental de masa abdominal en mesogastrio. Se le realiza resección de intestino delgado por sospecha de absceso con síndrome adherencial. El estudio patológico de la pieza quirúrgica demostró compromiso por linfoma no Hodgkin T monomórfico CD56+. Los linfomas T del tubo digestivo son inusuales; corresponden al 5% de las neoplasias linfoides de esta localización. El linfoma intestinal T monomórfico CD56+ corresponde a 10-20% de los linfomas T intestinales. Se presenta en regiones donde la enfermedad celiaca es infrecuente y no se asocia a enteropatía. Su curso es agresivo y habitualmente se manifiesta como una emergencia quirúrgica por obstrucción o perforación intestinal.

80 year old woman with incidental finding of abdominal mass in midgut, in which small bowel resection is performed for suspected abscess associated to surgical adhesions. Pathological examination of the surgical specimen showed a monomorphic CD56+ T cell lymphoma. T-cell lymphomas of the digestive tract are rare, accounting for 5% of all lymphoid neoplasms in this location. Monomorphic CD56+ intestinal T cell lymphoma corresponds to 10 - 20% of T cell intestinal lymphomas. This tumor occurs in regions where celiac disease is rare and it is not associated with enteropathy. Its course is aggressive and usually manifests as a surgical emergency by intestinal obstruction or perforation.

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Citas

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Derechos de autor 2015 Revista de la Facultad de Medicina

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Esta obra está bajo una licencia Creative Commons Reconocimiento 3.0 Unported.

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